For those who are newly diagnosed. Helpful information about scleroderma and the Foundation.
It is estimated that 90% of individuals with systemic sclerosis (SSc) have some evidence of pulmonary disease. This makes pulmonary disease second only to esophageal disease as the most common manifestation of SSc.
Pulmonary hypertension (PH) is high blood pressure in the blood vessels of the lungs. If the high blood pressure in the lungs is due to narrowing of the pulmonary arteries leading to increased pulmonary vascular resistance, it is known as pulmonary arterial hypertension (PAH).